Anomalous Systemic Supply of the Left Lower Lobe Without Sequestration: A Case Report

Abstract

A 2 year old boy presenting with tachypnea and dyspnea was diagnosed with anomalous supply of the left lower lobe on CT Scan. Chest CT was suggestive of an Arterio-venous malformation at the lower left lobe and a patent bronchus supply. The operative findings were of a large anomalous vessel originating from the descending thoracic aorta and supplying the lower left lobe of the lung, in addition to the left pulmonary artery branch with multiple large collateral veins converging on the inferior pulmonary vein. The post-operative period was uneventful. Systemic supply of a lung lobe in the absence of sequestration is a rare congenital malformation on the lung sequestration spectrum. Isolated tachypnea is an unusual presentation of this condition, with hemoptysis being the most common symptom.